A Case Report on Hirayama Disease

Cervical myelopathy affects the dorsal side of the cervical cord as a result of flexion action. Hirayama Disease is a non-progressive juvenile spinal muscular atrophy of the distal upper limb. It’s a benign motor neuron disease with a slow progression that eventually plateaus. In flexion, magnetic resonance imaging is more sensitive to these findings, which may be ignored in the neutral position. Hirayama illness is characterised by weakness and atrophy of the distal region of the upper limbs in adolescents and young adults. We present the case of a teenage boy who presented with asymmetrical weakness in both hands and whose magnetic resonance imaging (MR) in flexion revealed Hirayama disease-like changes.

Author (S) Details

B. B. Sharma
Department of Radio-diagnosis, SGT Medical College & Research Institute, Gurugram (Haryana), India.

Shashi Sharma
Department of Pediatrics, SGT Medical College & Research Institute, Gurugram (Haryana), India.

Monu Sarin
Department of Radio-diagnosis, SGT Medical College & Research Institute, Gurugram (Haryana), India.

Abhivind Bhutani
Department of Radio-diagnosis, SGT Medical College & Research Institute, Gurugram (Haryana), India.

Surabhi Lathwal
Department of Radio-diagnosis, SGT Medical College & Research Institute, Gurugram (Haryana), India.

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